抄録
This report is thought to be the first documented case of Klippel-Trenaunay syndrome complicated with omental hemorrhage with symptoms of acute abdomen. This 6-year-old Japanese girl was successfully treated by the extirpation of omental hemangioma in an emergency laparotomy. The association of the varicose vein, soft tissue and bony hypertrophy, and cutaneous hemagioma of the “port-wine” variety, confined to one extremity, was first described in 1900 by Klippel and Trenaunay1). After reporting three additional cases in 19072), Parkes-Weber3) described a second entity which appears to be similar to the Klippel-Trenaunay triad, with the addition of an arteriovenous fistula. Subsequently, there has been much confusion regarding both Klippel-Trenaunay and Parkes-Weber syndromes. Mullins4) described the syndrome as a Klippel-TrenaunayWeber syndrome and gave the name of “Naevus vasculosus osteohypertrophicus” to it. In 1965, Lindenauer5) reported an excellent survey on the syndrome, and advocated the separation of the Klippel-Trenaunay syndrome from the Parkes-Weber syndrome, because this differentiation is meaningful, both in terms of etiology and management. Many cases of the two entities were reported in the world. Three cases of the syndrome in Japan were first reported in 1927 by Tashiro6). Subsequently, many cases were reported and an excellent survey of 96 cases reported in Japan was made in 1966 by Fujisawa et al.7) The purpose of this paper is to report a Klippel-Trenaunay syndrome complicated with omental hemangioma with acute hemorrhage and with symptoms of acute abdomen.
