1979 年 18 巻 3 号 p. 218-222
The findings of computed tomography on Fukuyama type congenital muscular dystrophy were presented. They included low density area in the cerebral white matter with cortical atrophy. The pathologic examination of autopsied brain, on the other hand, revealed agyria and micropolygyria of the cerebral and/or cerebellar cortices, and maldevelopment and poor formation of the myelin in the cerebral white matter and pyramidal tracts in the brain stem. These pathologic alterations were considered to indicate a dysgenetic or dysplastic process, occurring in early uterine life. Intimate correlation between CT findings and neuropathologic observations of the brain was mentioned. Repeated CT examination would be convenient for taking care of these patients.
