抄録
After being taken with palpitation and then grand mal seizure at the age of 37 this patient had complained of myoclonic twitching of his whole body until his death of at the age of 60 and 8 months and had suffered from motor paralysis of the left side of the body at the age of 57 and 59.
In 4 of the patients children, the same myoclonic twitching has been found. An autopsy of this case showed encephalomalacies and / or hemorrhagic softenings of the claustrum and the lateral part of the putamen of both cerebral hemisphere, the subcortical white matter of the lobules parentralis, prouneus and cuneus of the right hemisphere and the right medial lemniscus. The symptoms of this case are attributed not to degenerative as in so-called myoclonus epilepsy, but to focal vascular lesions, following those many old and new hemorrhages.
