抄録
Budd-Chiari syndrome is a rare condition, which is thought to affect a couple of hundred patients in Japan per year. It is defined as portal hypertension owing to occlusion or stenosis of main hepatic vein or IVC intrahepatic portion. We will discuss this entity and write about our recent case. Budd-Chiari syndrome is divided into three categories: hepatic type, IVC type, or mixed type. The main strategy to treat this condition used to be medical management, or making shunts. But, recently TIPS, PTA, and transplantations are available. Among them IVR is coming to be the procedure of choice. Therefore we have to know about this condition.