Abstract
We experienced a case of congenital cystic adenomatoid malformation (CCAM) of the left lung with intralobar pulmonary sequestration in a 3-month-old boy. Antenatal ultrasonography at 22 weeks of gestation showed a multiple cystic lesion of the left lung. A multiple cystic lesion in the lower portion of the left lung was identified on chest radiography and computed tomography at birth. The infant developed no immediate signs of respiratory distress after birth. At 3 months of age the infant underwent left lower lobectomy because of enlargement of the cystic lesion. The specimen had an aberrant artery originating from the descending aorta and cystic lesion. Histopathologic examination showed a type II CCAM with a diameter of 4-5mm intralobar pulmonary sequestration.