A case of mucoepidermoid carcinoma of the larynx is reported. The patient was a 63-year-old man who had suffered from sore throat for nine months. By physical examination, swelling in the right epiglottis and arytenoid was noted. Histopathological findings of the specimen showed a mucoepidermoid carcinoma (low grade malignancy). The patient had chemotherapy and radiotherapy. Among malignant tumors of the larynx, mucoepidermoid carcinoma seemed to be extremely rare. Only seven cases of the laryngeal mucoepidermoid carcinoma including this case have been reported in our country. A pertinent literature was reviewed in this paper.