Abstract
Small aorta syndrome (SAS), which express the same meaning “Hypoplastic aortoiliac syndrome,” is an atherosclerotic occlusive disease. SAS has presented a wide range of hypoplasia from abdominal aorta to common iliac artery, particularly in young woman. Myotonic dystrophy is autosomal dominant multisystem disorder with several symptoms, presenting progressive muscular weakness. A 48-year-old woman, complicating with myotonic dystrophy, had complained of right leg pain at rest. MRA revealed severe stenosis in both the right common iliac, the superficial femoral artery and the left superficial femoral artery. We selected EVT for this lesion. At first, PTA ballooning was performed in right superficial femoral artery, and a stent was placed to the right common iliac artery. We experienced the rare case of SAS with myotonic dystrophy.