抄録
Erdheim-Chester disease is a rare non-Langerhans form of histiocytosis. We report the case of a 40-year-old man who presented with bone pain. Both femurs showed diffuse and symmetrical sclerosis on plain radiographs, CT, and Gd-MRI. Specimens obtained on open biopsy fulfilled the criteria of Erdheim-Chester disease. The patient was treated with prednisolone (20mg/day), methotrexate (7.5mg/week), and bisphosphonate (5mg/day), and has achieved a sustained clinical response.
