A case of alveolar soft part sarcoma of the nasal cavity

Abstract

Alveolar soft part sarcoma is considered an extremely rare disease and its tissue origin remains unclear. We report a case of alveolar soft part sarcoma that developed in the nasal cavity. The patient was a 41-year-old man who initially presented to our hospital with right nasal bleeding. A tumor had arisen in the right nasal cavity. Tumor excision was performed under local anesthesia. The histopathological diagnosis was alveolar soft part sarcoma, due to the presence of alveolar structures composed of polygonal cells and PAS-positive diastase-resistant crystals. Additional excision of the surrounding tissues was performed under general anesthesia. There has been no evidence of local recurrence or distant metastasis in the 5 years since the operation.