Follicular dendritic cell sarcoma (FDCS) is a rare malignancy arising from the follicular dendritic cells, which are antigen-presenting cells in the lymphoid follicles. We report the case of a 71-year-old male patient who was diagnosed as having FDCS of the tonsil. The patient presented with a 1-month history of throat pain and swelling of the right tonsil. An incisional biopsy of the tumor in the right tonsil was performed, and the diagnosis of FDCS was made on the basis of the histopathological and immunohistochemical findings. The tumor was surgically resected with the right pharyngeal wall by the pull-through method. A tensor fascia lata flap was used for reconstruction of the pharyngeal wall. No postoperative therapy was adopted. The swallowing function and articulation were preserved as prior to the surgery. At present, one year after the surgery, the patient has shown no evidence of either local recurrence or distant metastasis.
