抄録
A 36-year-old female with aortic arch syndrome had sudden bilateral hearing loss and tinnitus without vertigo. Since then, pure-tone audiometry has been repeated for over 10 years. During the period, vertigo was not observed and the hearing disturbances, which were improved temporarily by administration of predonisolone, fluctuated and slowly progressed. Finally, the hearing on the right was completely lost. There were marked similarities among the present patient and 2 patients with sensorineural hearing loss attributed to the aortic arch syndrome, which had been reported by other authors.