2020 Volume 53 Issue 2 Pages 147-153
It is extremely rare for hepatocellular carcinomas to occur in patients with glycogen storage disease. Here, such a case is reported. The patient, a 37-year-old man, was given a diagnosis of hepatocellular carcinoma occupying the right lobe, by CT. A diagnosis of glycogen storage disease had been given in his childhood. Because the tumor extended to the orifice of right, middle hepatic vein, and inferior vena cava, and was considered to be unresectable, he underwent transcatheter arterial chemoembolization. As a result, the size of the tumor was reduced from 11 cm to 7 cm. Right hepatectomy was performed. The volume of blood loss was 850 ml, and the operative time was 493 minutes. The patient experienced two postoperative complications possibly due to his glycogen storage disease. Severe lactic acidosis was treated with high concentration glucose administration on the 2nd postoperative day. Moreover, intraperitoneal bleeding from bilateral inferior phrenic arteries possibly due to the thrombocyte malfunction was stopped with transcatheter arterial embolization on the 6th postoperative day.
