抄録
Beckwith-Wiedemann syndrome (BWS) is a congenital disease characterized by exomphalos, macroglossia and gigantism. This paper presents a case of BWS undergoingtongue reduction at the age of six years. The patient was a three-month-old baby referredto our clinic for macroglossia from the Department of Pediatrics, Kagoshima University Hos-pital. His tongue showed hemihypertrophic macroglossia on the right side with only slightdifficulty in secretion. In our case, macroglossia induced prognathism and openbite as thepatient became older. We therefore feel that tongue reduction should be performed at theage of about one year and six months for congenital macroglossia.
