抄録
Hand-Schüller-Christian disease is a non-tumorous disease of the reticuloendothelial system characterized by the three features of bone defects, diabetes insipidus, and ocular proptosis. This disease has no definite cause and is generally called histiocytosis X, together with eosinophilic granuloma and Letterer-Siwe disease.
A 39-year-old man with extensive Hand-Schüller-Christian disease in the mandible, skull, and ilium was treated surgically for the mandible and with steroidal pulse therapy for the skull and ilium. After therapy, regeneration of the mandible and skull was observed without recurrence, and the patient showed satisfactory progress.