Meningiomas are a common histological type of brain tumor, but they are rarely found as primary extracranial tumors without intracranial lesions. A 62-year-old woman developed primary extracranial meningioma in the frontal sinus and subcutaneous forehead. Her prior ENT suspected frontal sinusitis and administered treatment, but no improvement was observed. They biopsied the lesion and diagnosed it as meningiothelial meningioma. The patient was then referred to the neurosurgery department at our hospital for evaluation of intracranial lesions. As there was no intracranial tumor, neurosurgery doctors followed up with MRI once a year. During the 4 years of follow up, the forehead protrusion gradually increased in size. Neurosurgery doctors referred her to us to improve her appearance. However, it was almost impossible to remove all of the tumor because infiltration had spread to the skin and skull base. Therefore, we resected the subcutaneous part of the tumor to improve her appearance. After the resection, her appearance improved and no re-growth of the tumor has been observed. However, careful long-term follow-up is necessary.
