Abstract
Follicular dendritic cell sarcoma (FDCS) is an uncommon neoplasm arising from follicular dendritic cells, which are antigen-presenting cells in lymphoid follicles.
A 65-year-old man had visited another hospital because of swelling of his left neck. Seven months later, a histopathological diagnosis of FDCS was made based on an incisional biopsy and so he was referred to our hospital for treatment.
The tumor was 45 mm in diameter, located in the accessory chain area and invading the skin over sternocleidmastoid muscle. A total excision with wide margins was performed and microscopically the surgical margin was free of tumor infiltration. He remains disease-free more than 2 years after surgery without chemotherapy or radiotherapy.
FDCS is considered to have a low to intermediate malignant potential, with a reported local recurrence rate of 23-43% and a distant metastasis rate of 21-24%. Clinical follow-up for local or distant relapse should be continued for years.
