A case of Klippel-Trenaunay-Weber disease in a 7 year old boy who presented with chronic ulcer and hypertrophy of the left leg, congenital arterio-venous fistula, elevated 0.2 saturation of venous blood, and hemangioma was reported. After recision of chronic ulcer and hemangioma, the cutaneous and subcutaneous defect was filled up with gastrocnemius muscle flap and was covered by skin graft. Postoperative course was uneventful with normal function of the left leg. The pathological diagnosis of this case was hemangioendothelioma, although the hemangioma of Klippel-Trenaunay-Weber disease usually shows a simple or cavernous hemangioma. The muscle flap technique which was preserved the cooperating skeletal muscle, is a useful method in children to expect the complete healing healing of chronic leg ulcer.
