The patient was transfered to Sendai Red Cross Hospital with an umbilical tumor from which urine overflowed. A catheter which was introduced in to the urethra came out through the umbilical tumor. A radical excision of the fistula was successfully performed 20 hours after birth. Postoperative diagnosis was a vesicoumbilical fistula with agenesis of the urachus. Pathogenesis and classfication of congenital disorders of the urachus have been discussed.
