A six-month-old boy with a tail attached immediately to the right of the anus was reported. The tail was 3.5cm long and its diameter was 1.5cm at the base. A hemangioma was noted at its base. Neither bone nor cartilage could be appreciated in it. It exhibited no spontaneous motion. At surgery, the tail was found to have a central muscular core which connected to the external anal sphincters. Histologic examinations demonstrated skin, adipose tissue, nerve fiber and a small amounts of skeletal muscle.