A 5-month-old baby was admitted to Tohoku University Hospital with complaint of right abdominal tumor. Multiple, various-size cysts were observed by ultrasonogram and computerized axial tomograrn. High blood pressure, 180/108mmHg, microscopic haematuria, and abnormal LDH level were observed in this patient. Right nephrectomy was performed under the diagnosis of multilocular cyst of the kidney. Microscopic examination disclosed that the tumor have blastoma cells in the tumor and diagnosis of cystic partially differentiated nephroblastoma was made.
