The incidense of congenital intestinal atresia and stenosis is about one from every 5,000 births. Eighteen cases with congenital intestinal atresia and stenosis have been treated in our department from April, 1972 to October, 1985. Of the eighteen cases, there are seven duodenal stenoses, four jejunal atresias, two jejunal stenoses, three ileal atresias, an ileal stenosis and a colon atresia. Five of the seven duodenal stenoses are annular pancreas. Three of the four jejunal atresias are apple-peel type of atresia. Two cases with ileal atresia, which had polypoid protrusion within the distal ileum, are considered to be caused by fetal intussusception. Although Down's syndrome is often associated with duodenal atresia and stenosis, only one cas was associated with Down's syndrome in our series. Although five cases (28%) have been died of congenital heart disease, idiopathic respiratory distress syndrome and anastomotic insufficiency, two cases with ileal atresia complicated with meconium peritonitis are alive and well.
