Right aortic arch (RAA) was recognized in 18 of 571 patients with congenital heart disease. The main branches of RAA showed mirror image branching in all patients. The heart diseases associated with RAA consisted of TOF (10 patients), VSD with PS (3 patients), VSD with PA (3 patients), cor biloculare with PA (1 patient), and type I truncus artriosus (1 patient). RAA was thus found to be frequently associated with VSD and anomalies of the right ventricular outflow tract. Palliative surgery was performed in 9 patients. Blalock-Taussing operation was performed in 5 potients with TOF and in 3 patients with PA. One patient died of hypoxia. Brock procedure was conducted in 1 patient with TOF. In 14 patients, radical surgery was performed. Total correction for TOF was performed in 10 patients. Two patients died of low cardiac output syndrome. In 3 patients with VSD and PS, infundibular resection and closure of VSD were performed. In 1 patient with truncus arterious, Rastelli procedure was performed, but the patient died of a respiratory failure.
