抄録
Congenital dilatation of biliary duct with anomalous pancreatico-biliary ductal junction was found in one of a monozygotic twins. The patient was the second baby of the twins with a birth weight of 2,190 g. She developed abdominal pain and vomiting at the age of 2-year-old. Endoscopic retrograde cholangio-pancreatogram revealed cogenital dilatation of biliary duct with anomalous pancreatico-biliary ductal junction. She underwent resection of the dilated extrahepatic biliary duct and gallbladder and hepatico-jejunostomy with Roux-en-Y anastmosis. Endoscopic retrograde cholangio-pancreatogram on the older sister showed normal pancreatico-biliary ductal junction. Genetic factors may have little importance for the causes of the disease in this case.
