Extensive Aganglionosis (正常神経節小腸55cm)の1例 : Extensive Aganglionosisに対する治療法の検討

抄録

This report concerns a case of an extensive aganglionosis having only 55cm of ganglionic jejunum below the ligament of Treitz. Five laparotomies were conducted, including the jejunostomy at 17 days of age, and the definitive operation by the Martin's method at 1 year and two months age. Intravenous hyperalimentation was applied for 3 years and 8 months, starting at 14 days of age. the patient, 7 years old at present, maintains 10% growth through oral intake alone and leads a normal social life. Based on the examination of postoperative bowel movement and capacity of absorption, the surgical managements we employed in our case can be regarded as one of the effective methods in extensive aganglionosis having ganglionic intestine shorter than 70cm from the ligament of Treitz.