A 4-Year-old female was admitted to Osaka University hospital with an episode of epigastralgia. On admission, laboratory data showed high levels of serum amylase, GOT and GPT. Several diagnostic procedures, especially abdominal echography and CT-scan, revealed dilated common bile duct. Under the diagnosis of congenital dilatation of the bile duct, laparotomy was carried out. Intraoperative cholangiogram showed cylindrically dilated bile duct and its anomalous communication with short ventral pancreatic duct. In a way, dorsal pancreatic duct could not be identified. So pancreatography from the minor papilla was carried out and it showed main dorsal duct which did not communicate with ventral pancreatic duct. Resection of the dile duct followed by hepatico-jejunostomy was performed. This rare case presented cylindrically dilated bile duct anomalously communicated with ventral pancreatic duct and complete pancreas divism.
