Abstract
A 0-day-old boy with congenital cystic adenomatoid malrformation (CCAM) of the lung is reported. Fetal ultrasonography showd multiple small cysts of the left lung, at the 20th gestational week. Sequnetial examinations revealed change of the characteristics of the lesion at 31st and 38th weeks in gestation. Agter birth, he developed no symptom. A large single cyst in the middle portion of the right lung, and multiple small cysts in the middle nad lower portion of the left lung were identified on plain chest X-ray and CT scans. The large cyst of the right lung and multiple small cysts in the middle portion of the left lung disappeared spontaneously on the 7th day of life. The multiple small cysts of the lower portion of the left lung got smaller, but were persisted. The scintigraphy revealed no function of the left lower portion. The left lower lobectomy of the lung was performedat the age of 17 days. The histological findings were consistent with those of CCAM Stocker type2. Seventeen cases of CCAM including our case have been reported, in which the antenatal findings of CCAM were compared with those of postanatal ones. Seven out of 17cases showed the taransformation during perinatal period. This fact is important to decide the timing of the surgery because the pulmonary lung diseases including CCAM and emphysematous diseases may decrease in size or disappear in the first fewmonths after birth.
