A Case of Epithelioid Inflammatory Myofibroblastic Sarcoma

Abstract

A 9-year-old boy was referred to our hospital for severe lower abdominal pain with inflammatory signs. Abdominal CT scans showed a 5-cm-size solid mass located near the sigmoid colon. Antibiotics administration failed to improve the inflammatory signs. On the basis of abdominal MRI, it was suspected that the tumor included hematoma, and he underwent laparoscopic single-site surgery. The solid tumor of 5.5×5.0×3.5 cm³ size located in the pelvic cavity was completely removed. Histopathological and genetic evaluation of the tumor confirmed epithelioid inflammatory myofibroblastic sarcoma (EIMS). Surgical resection is the most important treatment for EIMS because adjuvant therapy is less effective. The patient did not show any sign of recurrence within 2 years after surgery; however, he needs to be closely observed for a long time.