Abstract
A male neonate, weighting 2,755 g and without anus formation, was born by cesarean section. Since abdominal X-ray imaging showed giant colonic gas, he was suspected of having a congenital pouch colon (CPC). On day 1, emergency laparotomy was performed. The pouch-shaped colon with a colovesical fistula was identified. After the fistula was transected, a colostoma was formed on the pouchshaped colon. Stasis of feces in the pouch-shaped colon was evident, requiring manual irrigation several times a day. Following his transfer to our hospital, contrast enema revealed the existence of transverse and ascending colon, suggesting CPC type 3 according to the literature. During sacroabdominoperineal anorectoplasty, pull through was carried out using the rest of the colon with the pouch-shaped colon excised. On postoperative year 3, the patient still had frequent bowel movements, requiring medication or enema. Here, we present a rare case of CPC focusing on postoperative function of defecation.
