Abstract
The spontaneous perforation of a choledochal cyst is rare, and the treatment, including both single-stage and two-stage operations, is still controversial. We report the case of choledocal cyst perforation in a 1-year-old girl who was initially diagnosed as having intussusception. Repeated CT revealed a choledochal cyst and increased volume of ascites. Definite diagnosis was performed by laparoscopy; then, laparoscopic external cholecystostomy was performed for biliary drainage. As definitive surgery, excision of the choledochal cyst by Roux-en-Y hepaticojejunostomy was successfully performed 40 days after the drainage operation. We propose that two-stage operation including laparoscopic cholecystostomy is safe and reliable in the treatment of perforated choledochal cyst.