A Case of Two Points of Jejunal Membranous Atresia With Ectopic Pancreas

Abstract

A 1,616 g girl was born at 31 weeks and 5 days of gestation by emergency caesarian section because of fetal distress. Antenatal scanning had demonstrated intestinal atresia from 27 weeks of gestation. At birth, abdominal X-ray examination showed triple bubble signs. She was diagnosed as having jejunal atresia, which was decompressed using a nasogastric tube. The operation was carried out 3 days after birth. At laparotomy, two points of membranous atresia were found at 3 cm from the ligament of Treiz and further 3 cm distal. Partial enterectomy was carried out. Histopathological analysis showed that the proximal atresia point had type III ectopic pancreas according to the Heinrich classification. Until now, only one case of intestinal atresia with ectopic pancreas has been reported, but multiple types of only membranous atresia have never been reported. This case is considered to be extremely rare.