A rare case of complex spontaneous and induced nystagmus is reported. A 68-year-old man complained of vertigo when he turned his head to either side. In addition to jerky type congenital nystagmus, he showed a few remarkable features:1) Nystagmus was directed toward either the left or the right on central gaze.2) Nystagmus was sometimes accompanied by visually induced vertigo. 3) Nystagmus was influenced by head and neck position. These features suggest that congenital nystagmus was accompanied by visual vertigo and influenced by otolith and neck stimulation.