先天性骨形成不全症の1剖検例

張 相天; 佐藤 邦彦; 大橋 正典; 謝 啓掌; 神田 実喜男; 前田 徳尚; 黒川 光一; 岡部 長宏; 武藤 正之

doi:10.14930/jsma1939.30.101

AN AUTOPSY CASE OF OSTEOGENESIS IMPERFECTA CONGENITA

Souten Chou, Kunihiko Sato, Masanori Ôhashi, Keisho Sha, Mikio Kanda, Norihisa Maeda, Koichi Kurokawa, Nagahiro Okabe, Masayuki Muto

Author information

Souten Chou
Department of Patohlogy, School of Medecine, Showa University
Kunihiko Sato
Department of Patohlogy, School of Medecine, Showa University
Masanori Ôhashi
Department of Patohlogy, School of Medecine, Showa University
Keisho Sha
Department of Patohlogy, School of Medecine, Showa University
Mikio Kanda
Department of Patohlogy, School of Medecine, Showa University
Norihisa Maeda
St. Mrrianna Kai Toyoko Hospital
Koichi Kurokawa
St. Mrrianna Kai Toyoko Hospital
Nagahiro Okabe
St. Mrrianna Kai Toyoko Hospital
Masayuki Muto
St. Mrrianna Kai Toyoko Hospital

JOURNAL FREE ACCESS

1970 Volume 30 Issue 2 Pages 101-108

DOI https://doi.org/10.14930/jsma1939.30.101

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Abstract

This is a report of an autopsy case of osteogenesis imperf ecta congenita in male newborn infant a aged 27 days. In a case the lesions of bones showed imperfect enchondral and periostal osteogenesis, which may be due to the functional deficiency of the osteoblasts.
The hypoplasia of the thyroids and adrenals, and calcification of Hassall's bodies of the thymus are presented.
From these findings, a few relevant literatures are reviewed.

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