てんかんを呈する自己免疫性疾患　～自己免疫性てんかんの診断と治療～

抄録

ILAE classification of the epilepsies (2017) has adopted “immune” as one of the etiologies of epilepsy. Autoimmune epilepsy is regarded as a forme fruste of autoimmune encephalitis, where epileptic seizure is the sole or main feature of the disease. I will review the clinical characteristics of autoimmune epilepsy, practical diagnostic algorithm and score (without antibody testing), treatment and underlying autoimmune pathophysiology in this review. The earlier diagnosis and treatment impact the prognosis of this entity.