Dental Features and Clinical Approaches in Two Cases of Williams Syndrome

Abstract

We report some dental features and clinical approaches in two cases of Williams syndrome at the pediatric clinic of Kyushu University Hospital. Both cases had supravalvular aortic stenosis and mental retardation. Dental features included enamel hypoplasia, malocclusion and congenitally missing teeth.In case No.2, a cephalometric analysis showed that the lower jaw deviated to the front upper side with reverse occlusion. This case may have difficulty brushing his teeth due to functional disorders for spatial perception and micro-actuation. We believe that the treatment plan for case No.1 should consider the information from case No.2. Therefore, treatment should include the prevention of dental caries and periodontal disease, and carrying out the occlusal guidance by analyzing jaw and facial development.