Oro-Facial Findings and Masticatory Function in a Patient with Goldenhar Syndrome

Abstract

Goldenhar Syndrome is a congenital anomaly at the occurrence rate of 1 in 3,000-5,000 births. It is also known as Oculo-auriculo-vertebral dysplasia and characterized with triad of the dermoide or lipodermoide on the eye, auricular appendix and abnormality of the vertebral spine. The present findings of a fouryearold girl affected with the Goldenhar Syndrome, and who had undergone the dental caries treatment under the general anesthesia, were as follows.
1. Post-plastic surgical operation for macrostomia.
2. Bilateral eye dermoide and external ear hypoplasia.
3. Slight deformity of the vertebral spine.
4. Micrognathia and bird-like face.
5. Facial asymmetry and hypoplasia of the condyle in the mandible.