Dermoid cyst is a developmental anomaly that may be encountered infrequently in the soft tissues of the oral cavity. Intraoral dermoid cyst occurs most commonly in the midline of the floor of the mouth. Our purpose is to present a case, review the literature, and discuss this lesion's relationship to epidermoid cyst. A patient, a 9-year-old boy, was refferred to our clinic by his family dentist in January, 1980. Under general anesthesia, the cyst was extirpated through an intraoral incision. Sections of the specimen were embedded in paraffin and stained with hematoxylin and eosin. It was finally diagnosed as a sublingual epidermoid cyst by histologic examination.