Fronto-ethmoidal Encephalomeningocele

Abstract

A male child, born by normal spontaneous vaginal delivery, was noted to have a soft tumor, in the shape of an “elephant's nose, with a diameter of 2.5 cm×2.5 cm and 5.5 cm long in the inter-orbital region. With the diagnosis of naso-frontal type of fronto-ethmoidal encephalomeningocele with congenital hydrocephalus, corrective surgery was performed in two stages. At the first operation, a ventriculoperitoneal shunt and bilateral frontal craniectomy were performed, and closed with frozen human dura mater intracranially. Twenty days after the first operation, the encephalomeningocele was excised. The patient tolerated the surgery well.