Abstract
A boy was seen when he was 4 months old, because of an angioma characteristic of this syndrome and which was present the right preauricular region. Laboratory data showing decreased platelet count and fibrin, increased fibrin-fibrinogen degradation product, and so on were also characteristic. Light microscopy of a biopsied specimen revealed hemangioma tissue mainly composed of immature endothelial lumina with interstitial bleeding. Electron microscopic findings were also characteristic. Oral corticosteroid therapy and electron beam therapy of 9 MeV energy level, divided into three courses, were effective. The local findings and the laboratory data up to the complete cure are described. A comparison with criterion for DIC, was discussed.
