Recently, an extremely interesting case of melorheostosis was encountered at the Kagoshima prefectual Hospital for crippled children.
A review of the world literature failed to disclose similar marked progression of the disease.
Therefore this case is of sufficient interest to warrant a report.
The diagnosis is made from its characteristic roentgen appearance.
The charcteristic appearance resembling was flowing down the side of a candle is present in the streaked, sclerotic thickening on one side of the long bones of the limb.
The condition was first described in 1922 by Leni and joanny.
The patient was a boy of seven years old.
He was first seen in May 1968, at the age of seven, because of Pes calcaneus in the left limb, and the condition was found incidentally on roentgengrams.
Roentgenograms showed that in the left ilium, extending from the acetabulum upward, there was an irregular area of markedly increased density. The head of the femur the tibia, the fibula, and the tarsal bones, demonstrated similar sclerotic areas.
Abnormalities of the soft tissues of the affected limb, was found, including scleroderma.
Etiology and pathogenesis of Melorheostosis are unknown.
