Abstract
A case of primary fibrosarcoma of the calvarium is presented. A 51-year-old female was admitted because of a progressively enlarging mass in the left parietooccipital region. Radiograms of the skull revealed a radiolucent area with an osteosclerotic margin in the left parietooccipital region. CT scan showed an ovoid mass with osteolysis, extending both intracranially and extracranially. The tumor was slightly enhanced after infusion of contrast material. Under the diagnosis of a primary skull tumor, en bloc resection was performed. Histological diagnosis was fibrosarcoma. The postoperative course was uneventful. She was discharged without neurological deficits after completion of chemo- and radiotherapy. She was readmitted two months after discharge because of frequent coughing and hemoptysis. The patient died of pulmonary metastases 4 months after diagnosis.
 Primary fibrosarcoma of the calvarium is very rare. The literature suggests that definite surgical treatment should be done before distant metastases occur.