Hemimegaloencephaly with Periventricular Heterotopia —Case Report—

Shuichi SUGIYAMA; Masami FUJII; Sadahiro NOMURA; Tetsuo YAMASHITA; Haruhide ITO; Takashi HAYASHI

doi:10.2176/nmc.34.561

Shuichi SUGIYAMA, Masami FUJII, Sadahiro NOMURA, Tetsuo YAMASHITA, Haruhide ITO, Takashi HAYASHI

Author information

Keywords: hemimegaloencephaly, heterotopia, intractable seizure, magnetic resonance imaging

JOURNAL FREE ACCESS

1994 Volume 34 Issue 8 Pages 561-564

DOI https://doi.org/10.2176/nmc.34.561

Details

Abstract

A 7-year-old girl was admitted with an unusual anomaly of hemimegaloencephaly associated with periventricular heterotopia manifesting as intractable seizures and mental retardation. Magnetic resonance (MR) imaging showed left hemispheric hypertrophy and left ventricular dilatation. Proton density-weighted MR imaging revealed a periventricular lesion isointense with gray matter. MR imaging is an effective method for diagnosing hemimegaloencephaly and heterotopia.

Corresponding author

Register with J-STAGE for free!