We encountered 2 patients with Turner syndrome showing auditory disorders. The first patient noticed progressive hearing loss around the age of 20 years, and visited out department due to acute sensorineural hearing loss. She showed improvement after treatments similar to that for sudden sensorineural hearing loss. The second patient was a 5-year-old female with recurrent otitis media since the age of 3 years. After insertion of a tympanostomy tube, she was followed up in outpatient department.
Recurrent otitis media was suggested to be associated with brachycephaly due to cranial growth failure, high-arched palate, and impaired growth of the eustachian tube. Sensorineural hearing loss is considered to be due to damage in sensory hair cells and may develop at the lower age group, showing progression. Therefore, regular physical examinations, treatments, and hearing examinations are necessary in patients with Turner syndrome.
