顔面神経走行異常を伴った耳小骨奇形症例

抄録

We reported 3 cases of patients with congenital ossicular malformation and abnormal facial nerve pathway. In case 1, the facial nerve canal was absent and only the stapes head was observed below the facial nerve. The stapes was fixed and no surgical reconstruction was performed. In case 2, the facial nerve canal was absent and fibrous structure replacing the stapes was observed. The oval window was not existed and no surgical reconstruction was performed. In case 3, The long process of incus was connected to the stapes head with fibrous tissue. The facial nerve showed no bone defect and only the stapes head was observed below the facial nerve. Stapedial mobility was good and bone paste was used to connect the long process of the incus with the stapes head. After operation, hearing level improved and CT findings showed successful reconstruction of ossicular chain. Surgical techniques for ossicular reconstruction in patients with congenital ossicular malformation with abnormal facial nerve pathway were discussed.