Abstract
There have been only few reports with precise description of the prognosis of moyamoya disease. Therefore, we have conducted a long-term follow-up study of this disease especially on its clinical features. Fourty-one cases of moyamoya disease were analized on the onset of illness in detail. Twenty-seven cases were children and fourteen cases were adults.
According to the clinical type of onset, they were classified into 20 cases of ischemic attack, 5 cases of epileptic attack, 1 case of haemorrhagic attack and 1 case of other type in children, and 9 cases of haemorrhagic attack, 3 cases of ischemic attack and 2 cases of other clinical pictures in adults. Out of 41 cases, 36 cases have been followed for 2 years to 32 years. In five of them, various surgical vascular reconstruction was performed. Therefore, the remaining 31 cases were the materials of this follow-up study.
At the time of this follow-up study, there were 9 cases of normal daily activity, 3 cases of mental retardation, 2 cases of some neurological deficits and 6 cases of mental retardation plus some neurological deficits in children, and 6, 0, 4 and 1 cases respectively in adults.
The methods of vascular reconstruction were encephalo-myo synangiosis in 3 cases, encephalo-myo synangiosis plus STA-MCA anastomosis in one case and encephalo-myo synangiosis plus encephalo-duro-arterio synangiosis in one case. The result of surgical treatment is excellent in 3 cases.
