2010 年 31 巻 1 号 p. 59-63
We managed a male infant(1 year 9 months old, 87 cm, 13.2 kg) who was diagnosed with congenital long QT interval syndrome just after birth. Markedly long QT(QTc interval, 700 msec) was shown in electrocardiogram findings, and frequent torsades de pointes-type ventricular arrhythmia and non-sustained ventricular tachycardia were observed from birth. He was administered a combination of mexiletine and propranolol, after which arrhythmia disappeared and the QTc interval became stable at 420-450 msec. For ophthalmic surgery, we conducted total intravenous general anesthesia with remifentanil and propofol using laryngeal mask airway management. During the operation, HR was 100-110 bpm and non-invasive blood pressure was 80-100/35-40 mmHg, while the QTc interval was 460 msec without further QT lengthening.
