Congenitally Corrected Transposition of the Great Arteries Treated by Partial Systemic Ventriculectomy

Abstract

Congenitally corrected transposition of the great arteries (CCTGA) is a rare congenital heart disease characterized by atrioventricular (AV) and ventriculo-arterial discordance;¹ that is, the left ventricle supports the pulmonary circulation and the right ventricle supports the systemic circulation. The most common cardiac anomalies in CCTGA include ventricular septal defect, pulmonary outflow tract obstruction and abnormalities of the systemic AV valve. ¹ The dysfunction of the systemic ventricle occurs with increasing frequency in older patients with CCTGA, independent of their commonly associated structural defects.^2-4 We report a patient with CCTGA undergone the partial ventriculectomy for his systemic ventricular dysfunction. (Circ J 2003; 67: 354 - 356)