2022 Volume 64 Issue 2 Pages 164-171
A 75-year old male patient underwent consultation with his primary care physician for anorexia and jaundice. He was suspected to have IgG4-related sclerosing cholangitis (SC) and was treated with steroids. However, the patient did not improve, and he was referred to our hospital. Endoscopic retrograde cholangiopancreatography (ERCP) revealed numerous precipitates and irregularities in the distal bile duct wall. Bile cytology and culture identified Candida albicans, suggestive of biliary candidiasis. Subsequently, corticosteroids and antifungal drugs were administered, which ameliorated jaundice and other symptoms. He was diagnosed with IgG4-related SC as a quasi-confirmative diagnosis. Herein, we report a rare case of IgG4-related SC complicated with biliary candidiasis, as determined by cholangiography and bile cytology using ERCP.