Successful Treatment of Heart Failure in an Adult Patient with Prader-Willi Syndrome

Hiroaki Kawano; Tooru Ikeda; Koichi Shimazaki; Shuji Arakawa; Yuji Matsumoto; Motonobu Hayano; Koji Maemura

doi:10.2169/internalmedicine.52.8659

CASE REPORTS

Successful Treatment of Heart Failure in an Adult Patient with Prader-Willi Syndrome

Hiroaki Kawano, Tooru Ikeda, Koichi Shimazaki, Shuji Arakawa, Yuji Matsumoto, Motonobu Hayano, Koji Maemura

著者情報

キーワード: obstructive sleep apnea, central sleep apnea, obesity hypoventilation syndrome, rehabilitation, noninvasive positive pressure ventilation

ジャーナルオープンアクセス

2013 年 52 巻 7 号 p. 771-776

DOI https://doi.org/10.2169/internalmedicine.52.8659

詳細

抄録

Prader-Willi Syndrome (PWS) is a rare genetic disorder characterized by physical, psychological and physiological abnormalities. Obesity and related cardiovascular diseases are a common problem in adult patients with PWS. This report describes a case of adult PWS with heart failure associated with marked obesity and sleep-disordered breathing that was successfully treated with oxygen therapy, adaptive servoventilation, medications, diet therapy and rehabilitation.

責任著者(Corresponding author)

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