Internal Medicine
Online ISSN : 1349-7235
Print ISSN : 0918-2918
ISSN-L : 0918-2918
CASE REPORTS
An Iron-chelating Agent Improved the Cardiac Function in a Patient with Severe Heart Failure Due to Hereditary Hemochromatosis
Akito SetoguchiHiroaki KawanoShinji OkanoTomohiro HondaTakeharu KatoSumito DatekiAkira SenooYomi NakashimaTetsufumi MotokawaYuki UenoRyohei AkashiTsuyoshi YonekuraEijun SueyoshiSatoshi IkedaYasushi MiyazakiKoji Maemura
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ジャーナル オープンアクセス

2024 年 63 巻 2 号 p. 253-258

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A 24-year-old man was admitted to our hospital because of severe heart failure. Although he was treated with diuretics and positive inotropic agents, his heart failure progressed. An endomyocardial biopsy revealed iron deposition in his myocytes. Finally, he was diagnosed with hereditary hemochromatosis. After starting administration of an iron-chelating agent in addition to conventional treatment for heart failure, his condition improved. We should consider hemochromatosis in heart failure patients with severe right ventricular dysfunction in addition to left ventricular dysfunction.

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© 2024 by The Japanese Society of Internal Medicine

This article is licensed under a Creative Commons [Attribution-NonCommercial-NoDerivatives 4.0 International] license.
https://creativecommons.org/licenses/by-nc-nd/4.0/
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