A Case of Autoimmune Polyglandular Syndrome Type 3 Complicated with IgG4-related Disease

Yusuke Murata; Masaki Haneda; Norikazu Miyakawa; Saiko Nishida; Nobuhiro Kajihara; Sarie Maeda; Kaoru Ono; Satoko Hanatani; Motoyuki Igata; Yuki Takaki; Hiroyuki Motoshima; Hideki Kishikawa; Eiichi Araki

doi:10.2169/internalmedicine.1270-22

この記事には本公開記事があります。本公開記事を参照してください。
引用する場合も本公開記事を引用してください。

A Case of Autoimmune Polyglandular Syndrome Type 3 Complicated with IgG4-related Disease

Yusuke Murata, Masaki Haneda, Norikazu Miyakawa, Saiko Nishida, Nobuhiro Kajihara, Sarie Maeda, Kaoru Ono, Satoko Hanatani, Motoyuki Igata, Yuki Takaki, Hiroyuki Motoshima, Hideki Kishikawa, Eiichi Araki

著者情報

キーワード: Autoimmune pancreatitis, Autoimmune polyglandular syndrome, Type 1 diabetes mellitus, IgG4-related disease

ジャーナルオープンアクセス早期公開

論文ID: 1270-22

DOI https://doi.org/10.2169/internalmedicine.1270-22

この記事には本公開記事があります。

The final version of this article is now available: Vol. 63 (2024), No. 3 pp. 425-431

詳細

抄録

A 52-year-old Japanese woman developed type 1 diabetes mellitus (type 1 DM) at 41 years old. She became complicated with Hashimoto's disease and showed swelling of both submandibular glands, which was diagnosed as IgG4-related disease (IgG4-RD). This is a rare case of a Japanese patient with autoimmune polyglandular syndrome type 3A (APS-3A) coexisting with autoimmune thyroid disease (AITD) and type 1 DM complicated by IgG4-RD. Bilateral submandibular gland resection was successfully performed without steroid therapy. We discuss the possibility that the immunological pathogenic mechanisms of APS-3A and IgG4-RD are related.

責任著者(Corresponding author)

J-STAGEへの登録はこちら（無料）